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Essential Biochemistry - Hemoglobin Metabolism (Section 3 - No. 33)

Which enzyme is deficient in acute intermittent porphyria?
Uroporphyrinogen I synthase
Aminolevulinate dehydratase
Uroporphyrinogen III synthase
Ferrochelatase

Explanation

Uroporphyrinogen I synthase is deficient in acute intermittent porphyria.

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